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Table 1 Clinical and demographic features of the 20 SSc patients

From: Impaired Cav-1 expression in SSc mesenchymal cells upregulates VEGF signaling: a link between vascular involvement and fibrosis

Sex/Age (years)

Year of SSc onset

MRSS

Autoantibodies

Lung involvment HRCT/PFT

Heart and kidney involvement

Digital ulcers

F/22

2009

14

ANA/ACA

Normal/Normal

Normal/Normal

Yes

F/45

1998

13

ANA/ACA

Normal/Normal

Normal/Normal

Yes

M/43

1985

18

ANA/ACA

Normal/Normal

Normal/Normal

Yes

F/26

2003

8

ANA/ACA

Normal/Normal

Normal/Normal

Yes

F/39

1980

15

ANA/ACA

Normal/Normal

Normal/Normal

No

F/40

2002

8

ANA/ACA

Fibrosis/Normal

Normal/Normal

Yes

M/45

2000

10

ANA/ACA

Normal/Normal

Normal/Normal

Yes

F/21

2010

13

ANA/ACA

Normal/Normal

Normal/Normal

Yes

F/30

2000

9

ANA/ACA

Fibrosis/Normal

Normal/Normal

Yes

F/22

2008

11

ANA/ACA

Normal/Normal

Normal/Normal

Yes

F/40

1978

12

ANA/Scl-70

Normal/Normal

Normal/Normal

No

F/41

2001

10

ANA/Scl-70

Fibrosis/Normal

Normal/Normal

Yes

F/23

2007

13

ANA/Scl-70

Normal/Normal

Normal/Normal

Yes

F/46

2007

12

ANA/Scl-70

Normal/Normal

Normal/Normal

No

F/21

2007

13

ANA/Scl-70

Normal/Normal

Normal/Normal

Yes

F/31

2000

15

ANA/Scl-70

Normal/Normal

Normal/Normal

Yes

F/36

1999

20

ANA/Scl-70

Normal/Normal

Normal/Normal

Yes

F/20

2008

11

ANA/Scl-70

Normal/Normal

Normal/Normal

Yes

F/41

2004

20

ANA/Scl-70

Normal/Normal

Normal/Normal

Yes

F/30

2007

10

ANA/Scl-70

Normal/Normal

Normal/Normal

Yes

  1. ACA = anti-centromere antibodies ANA = antinuclear antibodies; HRCT = high resolution computed tomography; MRSS = modified Rodnan skin thickness score (maximum possible score 51); PFT = pulmonary function test.