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Table 2 Extrinsic mediators of fibroblast activity potentially implicated in SSc

From: Fibrosis in systemic sclerosis: common and unique pathobiology

Cytokines

TGF-β

IL-4

IL-13

IL-17

IL-33

Growth factors, peptides and bioactive lipids

Wnt family (Wnt3a, Wnt10b, others)

CTGF (matricellular protein)

PDGF

IGFBP-5

Endothelin-1

Adenosine

Lysophosphatidic acid (LPA)

Prostaglandin F

Chemokines

CXCL12

MCP-1

Autoantibodies

Antibody to Topo I

Anti-fibroblast antibody

Anti-PDGF antibody