From: Centrilobular emphysema combined with pulmonary fibrosis results in improved survival
Variable |
ES 0 (n= 48) |
0 < ES ≤ 2 (n= 26) |
ES > 2 (n= 28) | P value |
---|---|---|---|---|
Age years; median [1st, 3rd] | 62 [58, 68] | 61 [53, 67] | 57 [51, 62] | NS* |
Gender: | ||||
Male, n Female, n |
31 17 |
18 8 |
17 11 | NS† |
Race: | ||||
Caucasian, n | 38 | 15 | 16 | |
African-American, n | 8 | 9 | 11 | NS† |
Other, n | 2 | 2 | 1 | |
Medication: | ||||
Prednisone, n | 40 | 26 | 22 | NS† |
Azathioprine, n | 24 | 13 | 12 | NS† |
Mycophenolate, n | 14 | 9 | 4 | NS† |
N-Acetylcysteine, n | 22 | 13 | 7 | NS† |
ACE Inhibitor, n | 10 | 6 | 3 | NS† |
Statin, n | 20 | 14 | 11 | NS† |
Smoking: | ||||
Current smoker, n (%) | 1(2) | 2 (7) | 4 (14) | NS† |
Ever-smoker, n (%) | 27 (56) | 21 (81) | 24 (86) | < 0.01† |
Pack/years, median [ 1st, 3rd] | 5 [0, 20] | 20 [10, 39] | 40 [20, 50] | < 0.0001* |
Fibrosis score: | ||||
< 10%, n | 7 | 5 | 2 | |
10 - 40%, n | 27 | 16 | 19 | NS† |
> 40%, n | 14 | 5 | 7 | |
Right heart catheterization: | ||||
Performed, n (%) | 37 (77) | 22 (84) | 17 (61) | NS† |
Mean PAP mm Hg; median [ 1st, 3rd] | 21 [18, 24] | 29 [22, 40] | 29 [22, 33] | < 0.001* |
Surgical lung biopsy: | ||||
Performed, n (%) | 36 (75) | 17 (65) | 20 (71) | NS† |
UIP, n | 32 | 14 | 14 | NS† |
Fibrotic NSIP, n | 4 | 3 | 6 | |
Lung transplantation performed, n (%) | 19 (39) | 6 (23) | 9 (32) | NS† |